Abstract
This report describes a neonate with congenital partial absence of the pericardium associated with hypoplastic left heart syndrome. The patient presented with severe heart failure caused by a hypoplastic left ventricle. The infant died at 15 hours of age because of intractable congestive heart failure. Necropsy revealed, in addition to a hypoplastic left ventricle, a transverse biventricular constriction suggestive of partial absence of the pericardium. In addition to cardiovascular malformations, a left hydronephrosis and a bicornuate uterus was found. We report a rare clinical entity and review the literature.
Original language | English (US) |
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Pages (from-to) | 121-123 |
Number of pages | 3 |
Journal | American Journal of Perinatology |
Volume | 20 |
Issue number | 3 |
DOIs | |
State | Published - Apr 2003 |
Externally published | Yes |
All Science Journal Classification (ASJC) codes
- Pediatrics, Perinatology, and Child Health
- Obstetrics and Gynecology
Keywords
- Congenital partial pericardial defect
- Hypoplastic left heart syndrome
- Neonate