Physical management of patients with neuromuscular diseases

John R. Bach, Priya Bolikal

Research output: Chapter in Book/Report/Conference proceedingChapter

Abstract

In the current economic climate in which it is no longer practical for a patient with neuromuscular disease to routinely be evaluated by specialists in orthopedics, cardiology, pulmonary medicine, neurology, nutrition, physical and occupational therapy, speech and language pathology, and physiatry, a neuromuscular disease practitioner needs to be capable of understanding and managing 90 % of these domains. Patients' ambulation can often be prolonged by judiciously eliminating lower limb contractures, repositioning muscles, targeted physical therapeutic interventions, and medical therapy. Children with spinal muscular atrophy type 1 (SMA1) can live into adulthood without tracheostomy tubes despite requiring continuous ventilatory support from 4 months of age. Patients with Duchenne muscular dystrophy (DMD) can live into their late 40s without tracheostomy tubes despite continuous ventilator dependence for over 25 years. Twenty-five to over 40 % of amyotrophic lateral sclerosis (ALS) patients can survive for an average of 1 and up to 8 years without tracheostomy tubes despite requiring continuous ventilatory support. All of these advances require knowledge of skeletal and respiratory muscle interventions. While critical for quality of life and to prolong life, they are little understood by the medical community.

Original languageEnglish (US)
Title of host publicationNeuromuscular Disorders in Clinical Practice
PublisherSpringer New York
Pages327-340
Number of pages14
Volume9781461465676
ISBN (Electronic)9781461465676
ISBN (Print)1461465664, 9781461465669
DOIs
StatePublished - Nov 1 2014

All Science Journal Classification (ASJC) codes

  • Medicine(all)

Keywords

  • Mechanically Assisted Coughing
  • Neuromuscular Disorders
  • Noninvasive Ventilation
  • Orthopedic Management
  • Physical Medicine
  • Rehabilitation
  • Respiratory Mangement
  • Survival

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