Unicuspid unicommissural aortic valve: An extremely rare congenital anomaly

Sukhjeet Singh, Puneet Ghayal, Atish Mathur, Margaret Mysliwiec, Constantinos Lovoulos, Pallavi Solanki, Facc Marc Klapholz, Facc James Maher

Research output: Contribution to journalArticlepeer-review

21 Scopus citations


Unicuspid aortic valve is a rare congenital malformation that usually presents in the 3rd to 5th decade of life—and usually with severe aortic stenosis or regurgitation. It often requires surgical correction. Diagnosis can be made with 2- or 3-dimensional transthoracic or transesophageal echocardiography, cardiac computed tomography, or cardiac magnetic resonance imaging. We report the case of a 31-year-old man who presented with dyspnea on exertion due to severe aortic stenosis secondary to a unicuspid unicommissural aortic valve. After aortic valve replacement, this patient experienced complete heart block that required the placement of a permanent pacemaker.

Original languageEnglish (US)
Pages (from-to)273-276
Number of pages4
JournalTexas Heart Institute Journal
Issue number3
StatePublished - Jun 11 2015

All Science Journal Classification (ASJC) codes

  • Cardiology and Cardiovascular Medicine


  • Aortic valve stenosis/congenital/etiology
  • Aortic valve/abnormalities/ultrasonography/unicuspid unicommissural
  • Complete heart block
  • Congenital/surgery/ultrasonography
  • Heart defects
  • Pacemaker
  • Permanent
  • Unicuspid aortic valve


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